Volume 1
Number 1 January 2017Lutembacher Syndrome
DOI: https://doi.org/10.70357/jdamc.2017.v0101.09
Ali Y1 , Khan IA2 , Saha P3 , Saha R4 , Wahiduzzaman M5 , Rahman T6
Abstract
Lutembacher syndrome a rare complex heart disease comprises ASD (secundum) with mitral stenosis. ASD (Secundum)usually congenital but may be iatrogenic during IAS puncture during PTMC procedure. MS usually rheumatic origin. OurPatient Mrs. Fulmala, 60 yrs. old, housewife, non hypertensive, non diabetic admitted in DAMCH cardiac unit on 10.11.12with the complaints of progressive respiratory distress for ten years, cough for 5 yrs, chest pain for 2 yrs. Initially shortness ofbreath was in NYHA class II & at present it in NYHA class-III. She had a previous history of rheumatic fever in earlychildhood. There was history of recurrent attack of rheumatic fever. Subsequently she developed MS from rheumatic carditis.ASD was congenital in origin. If diagnosis could be done earlier, surgical closure of ASD with replacement of mitral valvebears a good prognostic value. Our patient is in elderly age & already developed pulmonary hypertension, so operativeprocedure is not suitable. So, the patient should be kept in conservative treatment.
Keywords: Lutembacher syndrome, atrial septal defect, mitral stenosis, septum primum, septum secundum
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