Volume 10

Number 1 January 2026

Mayer-Rokitansky-Kuster-Hauser syndrome Type 2 or MURCS co-occurrence with Benign Ovarian Tumor – a tremendous case report

DOI: https://doi.org/10.70357/jdamc.2026.v1001.12

Parvin M1 , Ferdous J2 , Alam MI3 , Jahan SL4 , Alam MI5

Abstract

Mayer-Rokitansky-Kuster-Hauser syndrome (MRKHS) is a congenital condition characterized by aplasia of the vaginawith or without concurrent uterine and/or cervical aplasia.Between the two types ,type 2 or MURCS is a rare formincluding Mullerian agenesis,Renal agenesis and Cervicothoracic somite anomalies.A 17 years old virgin presentedwith feeling of heaviness and lump in abdomen for 6 months with history of primary amenorrhoea till the date anda diagnosed case of MRKH with normal female karyotype 46XX also having unilateral left sided renal agenesis andhistory of multiple surgery for congenital heart disease (TOF), repair of inguinal hernia and laparotomy for pelvicmass with biopsy taking. Evaluation of the patient suggests a tremendous presentation of MURCS association withbenign ovarian tumor. A review of the literature reveals no other cases of MRKH with these tremendous anomalieshaving history of corrected TOF and inguinal hernia as well as with co occurrence of a huge benign ovarian tumor.

Keywords: Mayer-Rokitansky-Kuster-Hauser syndrome, MURCS, Mullerian agenesis, Benign ovarian tumor


  1. Department of Gynaecological Oncology

    Bangladesh Medical University, Shahbag, Dhaka

  2. Professor & Chairman, Department of Gynaecological Oncology

    Bangladesh Medical University, Shahbag, Dhaka

  3. Resident, Department of Palliative Medicine

    Bangladesh Medical University, Shahbag, Dhaka

  4. Medical Officer

    Thana Health Complex, Tejgaon, Dhaka

  5. Assistant Professor, Department of Respiratory Medicine

    Diabetic Association Medical College, Faridpur

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Volume 10, Number 1 January 2026
Page: 55-58